Bicuspid aortic valve affects about one percent of the population. It is a frequent cause of aortic insufficiency, and is also associated with aortic root or ascending aortic aneurysms. Techniques for aortic repair in patients with aortic insufficiency have been standardized and can be performed with satisfactory long term results. Minimally invasive aortic valve surgery has expanded in recent years, offering patients benefits in terms of improved postoperative recovery and cosmetic results. The authors present a case of minimally invasive repair of a bicuspid aortic valve and ascending aortic aneurysm through the upper ministernotomy approach.